MT1621 doxecitine/doxribtimine APPROVED
Drug Profile
ModalitySmall molecule
RouteOral
Therapy AreaRare Disease
Peak Sales Est$300M
Formulations[]
Companies
UCB (ORIGINATOR)100%
Mechanism: Nucleoside therapy
Expert: Provides deoxycytidine and deoxythymidine to bypass enzyme deficiency
Everyday: Provides deoxycytidine and deoxythymidine to bypass enzyme deficiency
Targets: []
Programs (1)
IndicationStageKey StudyRegional Status
TK2 deficiencyFILEDPhase 3[]
Notes
Deoxynucleoside substrate enhancement therapy for thymidine kinase 2 (TK2) deficiency, a mitochondrial DNA depletion syndrome. First potential treatment for this ultra-rare, fatal myopathy affecting children.
Data from Supabase · Updated 2026-03-24